Renal epithelioid angiomyolipoma: A case report

Rapidly Progressing Malignant Epithelioid Renal Angiomyolipoma: A Case Report.

INTRODUCTION Typical angiomyolipoma (AML) is a benign neoplasm, which consists of a mixture of smooth muscle, fat, abnormal blood vessels, and perivascular epithelioid cells, the latter of which have been described to be present in varying proportions. Recent reports have described renal masses comprised almost entirely of perivascular epithelioid cells and have designated them as “monotypic ep...

Huge retroperitoneal epithelioid angiomyolipoma: A case report

Angiomyolipoma (AML) is a type of tumor in the perivascular epithelioid cell neoplasm (PEComa) family. Epithelioid angiomyolipoma (EAML), having malignant potential, is considered a rare variant of angiomyolipoma. The most common site of EAMLs is kidney, and extra-renal EAMLs are very uncommon, with liver being the most common site.1 Other locations including retroperitoneum, uterus, liver, lun...

Renal epithelioid angiomyolipoma presenting clinically as renal cell carcinoma – A case report

A rare case of metastatic renal epithelioid angiomyolipoma.

SECOND OPINION Multidisciplinary Consultations on Challenging Cases The University of Colorado Denver School of Medicine faculty holds weekly second opinion conferences focusing on cancer cases that represent most major cancer sites. Patients seen for second opinions are evaluated by an oncologic specialist. Their history, pathology, and radiographs are reviewed during the multidisciplinary con...

Epithelioid angiomyolipoma: a rare variant of renal angiomyolipoma.

OBJECTIVE We present a case of primary renal epithelioid angiomyolipoma, its association with tuberous sclerosis and review the literature. METHODS We present the case of a 12 year-old male with past medical history of tuberous sclerosis, characterized by developmental delay, tonic and clonic seizures, and cutaneous abnormalities. He presented with macroscopic hematuria and abdominal pain. CT...